BH4 - Literature





GTPCH	GFRP	PTPS	SR	PCD	DHPR

Literature : 2006

Literature 2006
1.	Thöny, B. and N. Blau (2006). BIOMDB: Database of mutations causing tetrahydrobiopterin deficiencies. PKU and BH4: Advances in Phenylketonuria and Tetrahydrobiopterin. Heilbronn, SPS Verlagsgesellschaft: 707-713.
2.	Blau, N. and J. L. Dhondt (2006). BIODEF: International database of tetrahydrobiopterin deficiencies. PKU and BH4: Advances in Phenylketonuria and Tetrahydrobiopterin. Heilbronn, SPS Verlagsgesellschaft: 701-706.
3.	Blau, N. (2006). Nomenclature and laboratory diagnosis of tetrahydrobiopterin deficiencies. PKU and BH4: Advances in Phenylketonuria and Tetrahydrobiopterin. Heilbronn, SPS Verlagsgesellschaft: 555-567.
4.	Boneh, A., D. E. Francis, M. Humphrey, H. J. Upton and H. L. Peters (2006). "Three-year audit of the hyperphenylalaninaemia/phenylketonuria spectrum in Victoria." J Paediatr Child Health 42(9): 496-8.
5.	Foxton, R. H., J. M. Land and S. J. Heales (2006). "Tetrahydrobiopterin Availability in Parkinson's and Alzheimer's Disease; Potential Pathogenic Mechanisms." Neurochem Res. Epub ahead of press
6.	Sedel, F., M. J. Ribeiro, P. Remy, N. Blau, J. M. Saudubray and Y. Agid (2006). "Dihydropteridine reductase deficiency: levodopa long term effectiveness without dyskinesia." Neurology 67: 2243-45.
7.	Qu, Y., F. Song, H. Wang and Y. Jin (2006). "Detection of the prevalent mutations of 6-pyruvoyl-tetrahydropterin synthase gene by PCR-RFLP analysis in Chinese patients." Zhonghua Yi Xue Yi Chuan Xue Za Zhi 23(6): 680-2.[Article in Chinese]
8.	Kontostavlaki, D. P., M. T. Panayotacopoulou, J. A. Sluijs, U. A. Unmehopa, I. Huitinga, E. M. Hol and D. F. Swaab (2006). "Co-Expression of Tyrosine Hydroxylase and GTP Cyclohydrolase I in Arginine Vasopressin-Synthesizing Neurons of the Human Supraoptic Nucleus Demonstrated by Laser Microdissection and Real-Time PCR." Neuroendocrinology. Epub ahead of press
9.	Forstermann, U. (2006). "Janus-faced role of endothelial NO synthase in vascular disease: uncoupling of oxygen reduction from NO synthesis and its pharmacological reversal." Biol Chem 387(12): 1521-33.
10.	Ohta, E., M. Funayama, H. Ichinose, I. Toyoshima, F. Urano, M. Matsuo, N. Tomoko, K. Yukihiko, S. Yoshino, H. Yokoyama, H. Shimazu, K. Maeda, K. Hasegawa and F. Obata (2006). "Novel Mutations in the Guanosine Triphosphate Cyclohydrolase 1 Gene Associated With DYT5 Dystonia." Arch Neurol 63(11): 1605-1610.
11.	Zurflüh, M. R., L. Fiori, B. Fiege, N. B. Kuru, M. Demirkol, K. H. Gärtner, B. Thöny, M. Giovannini and N. Blau (2006). "Pharmacokinetics of orally administered tetrahydrobiopterin in patients with phenylalanine hydroxylase deficiency." J Inherit Metab Dis 29(6)725-731
12.	Gogonea, V., J. M. Shy, 2nd and P. K. Biswas (2006). "Electronic Structure, Ionization Potential, and Electron Affinity of the Enzyme Cofactor (6R)-5,6,7,8-Tetrahydrobiopterin in the Gas Phase, Solution, and Protein Environments." J Phys Chem B Condens Matter Mater Surf Interfaces Biophys 110(45): 22861-22871.
13.	Friedman, J., K. Hylan, N. Blau and M. Maccollin (2006). "Dopa-responsive hypersomnia and mixed movement disorder due to sepiapterin reductase deficiency." Neurology 67: 2032-2035.
14.	Salard, I., E. Mercey, E. Rekka, J. L. Boucher, P. Nioche, I. Mikula, P. Martasek, C. S. Raman and D. Mansuy (2006). "Analogies and surprising differences between recombinant nitric oxide synthase-like proteins from Staphylococcus aureus and Bacillus anthracis in their interactions with l-arginine analogs and iron ligands." J Inorg Biochem 100(12): 2024-33.
15.	Tiemeier, H., D. Fekkes, A. Hofman, H. R. van Tuijl, A. J. Kiliaan and M. M. Breteler (2006). "Plasma pterins and folate in late life depression: the Rotterdam Study." Psychiatry Res 145(2-3): 199-206.
16.	Echenne, B., A. Roubertie, B. Assmann, T. Lutz, J. M. Penzien, B. Thony, N. Blau and G. F. Hoffmann (2006). "Sepiapterin reductase deficiency: clinical presentation and evaluation of long-term therapy." Pediatr Neurol 35(5): 308-13.
17.	Taylor, N. E., K. G. Maier, R. J. Roman and A. W. Cowley, Jr. (2006). "NO synthase uncoupling in the kidney of Dahl S rats: role of dihydrobiopterin." Hypertension 48(6): 1066-71.
18.	Tegeder, I., M. Costigan, R. S. Griffin, A. Abele, I. Belfer, H. Schmidt, C. Ehnert, J. Nejim, C. Marian, J. Scholz, T. Wu, A. Allchorne, L. Diatchenko, A. M. Binshtok, D. Goldman, J. Adolph, S. Sama, S. J. Atlas, W. A. Carlezon, A. Parsegian, J. Lotsch, R. B. Fillingim, W. Maixner, G. Geisslinger, M. B. Max and C. J. Woolf (2006). "GTP cyclohydrolase and tetrahydrobiopterin regulate pain sensitivity and persistence." Nat Med 12(11): 1269-77.
19.	Tachibana, S., M. Suzuki and Y. Asano (2006). "Application of an enzyme chip to the microquantification of l-phenylalanine." Anal Biochem 359(1): 72-8.
20.	Xie, H., Z. Y. Wu, N. Wang, Z. W. Li, M. T. Lin and S. X. Murong (2006). "[Clinical analysis of dopa-responsive dystonia and mutation analysis of the GCH I gene.]." Zhonghua Er Ke Za Zhi 44(7): 492-5. [Article in Chinese]
21.	El Yacoubi, B., S. Bonnett, J. N. Anderson, M. A. Swairjo, D. Iwata-Reuyl and V. de Crecy-Lagard (2006). "Discovery of a new prokaryotic type I GTP cyclohydrolase family." J Biol Chem 281(49): 37586-93.
22.	Weiss, D. J., M. Dorris, A. Loh and L. Peterson (2006). "Dehydrogenase based reagentless biosensor for monitoring phenylketonuria." Biosens Bioelectron. Epub ahead of press
23.	Petri, A., J. Ahnfelt-Ronne, K. S. Frederiksen, D. G. Edwards, D. Madsen, P. Serup, J. Fleckner and R. S. Heller (2006). "The effect of neurogenin3 deficiency on pancreatic gene expression in embryonic mice." J Mol Endocrinol 37(2): 301-316.
24.	Hoekstra, R., D. Fekkes, L. Pepplinkhuizen, A. J. Loonen, S. Tuinier and W. M. Verhoeven (2006). "Nitric Oxide and Neopterin in Bipolar Affective Disorder." Neuropsychobiology 54(1): 75-81.
25.	Ettl, A. K., J. Holzschuh and W. Driever (2006). "The zebrafish mutation m865 affects formation of dopaminergic neurons and neuronal survival, and maps to a genetic interval containing the sepiapterin reductase locus." Anat Embryol (Berl) 211 Suppl 7: 73-86.
26.	Pan, Y., Y. Berman, S. Haberny, E. Meller and K. D. Carr (2006). "Synthesis, protein levels, activity, and phosphorylation state of tyrosine hydroxylase in mesoaccumbens and nigrostriatal dopamine pathways of chronically food-restricted rats." Brain Res 1122(1): 135-42.
27.	Spoonamore, J. E., A. L. Dahlgran, N. E. Jacobsen and V. Bandarian (2006). "Evolution of New Function in the GTP Cyclohydrolase II Proteins of Streptomyces coelicolor." Biochemistry 45(39): 12144-55.
28.	Moens AL, Chakir K, Champion HC, et al. Tetrahydrobiopterin reverses established heart failure by recoupling of uncoupled endothelial NOS 3rd Annual Symposium of the American-Heart-Association-Council on Basis Cardiovascular Sciences, JUL 31-AUG 03, 2006 CIRCULATION RESEARCH 99 (5): E20-E20, SEP 1 2006
29.	Funderburk, C. D., K. M. Bowling, D. Xu, Z. Huang and M. O'Donnell J (2006). "Atypical N-terminal extensions confer novel regulatory properties on GTP cyclohydrolase isoforms in Drosophila melanogaster." J Biol Chem. Epun ahead of press
30.	Antoniades, C., C. Shirodaria, N. Warrick, S. Cai, J. de Bono, J. Lee, P. Leeson, S. Neubauer, C. Ratnatunga, R. Pillai, H. Refsum and K. M. Channon (2006). "5-methyltetrahydrofolate rapidly improves endothelial function and decreases superoxide production in human vessels: effects on vascular tetrahydrobiopterin availability and endothelial nitric oxide synthase coupling." Circulation 114(11): 1193-201.
31.	Pey, A. L., A. Martinez, R. Charubala, D. J. Maitland, K. Teigen, A. Calvo, W. Pfleiderer, J. M. Wood and K. U. Schallreuter (2006). "Specific interaction of the diastereomers 7(R)- and 7(S)-tetrahydrobiopterin with phenylalanine hydroxylase: implications for understanding primapterinuria and vitiligo." Faseb J 20(12): 2130-2.
32.	Morao, I., G. Periyasamy, I. H. Hillier and J. A. Joule (2006). "The role of tetrahydrobiopterin in catalysis by nitric oxide synthase." Chem Commun (Camb)(33): 3525-7.
33.	Kong, J. S., J. Y. Kang, H. L. Kim, O. S. Kwon, K. H. Lee and Y. S. Park (2006). "6-Pyruvoyltetrahydropterin synthase orthologs of either a single or dual domain structure are responsible for tetrahydrobiopterin synthesis in bacteria." FEBS Lett 580(20): 4900-4.
34.	Abeling, N. G. G. M., M. Duran, H. D. Bakker, A. E. M. Stroomer, B. Thöny, N. Blau and B. T. Poll-The (2006). "Sepiapterin reductase deficiency an autosomal recessive DOPA-responsive dystonia." Mol Genet Metab 89: 116-120.
35.	Engin, A. B., D. Tuzun and G. Sahin (2006). "Evaluation of pteridine metabolism in battery workers chronically exposed to lead." Hum Exp Toxicol 25(7): 353-9.
36.	Robson, S. K., M. Vickers, M. W. Blows and R. H. Crozier (2006). "Age determination in individual wild-caught Drosophila serrata using pteridine concentration." J Exp Biol 209(Pt 16): 3155-63.
37.	Wajima T, Shimizu S, Ishii M, et al. Reduction of myocardial infarct size by tetrahydrobiopterin: Possible involvement of mitochondrial K-ATP channels activation through nitric oxide production 79th Annual Meeting of the Japanese-Pharmacological-Society, MAR 08-10, 2006 JOURNAL OF PHARMACOLOGICAL SCIENCES 100: 223P-223P, Suppl. 1 2006 [Abstract]
38.	Hiroi T, Shimizu S, Ishi M, et al. Possible involvement of Jak2-STAT pathway on the stimulation of tetrahydrobiopterin synthesis by hydrogen peroxide in vascular endothelial cells 79th Annual Meeting of the Japanese-Pharmacological-Society, MAR 08-10, 2006 JOURNAL OF PHARMACOLOGICAL SCIENCES 100: 178P-178P, Suppl. 1 2006 [Abstract]
39.	Sasaki T, Shimizu S, Ishii M, et al. Basic fibroblast growth factor induces tetrahydrobiopterin synthesis through stimulation of Erk pathway in vascular endothelial cells 79th Annual Meeting of the Japanese-Pharmacological-Society, MAR 08-10, 2006 JOURNAL OF PHARMACOLOGICAL SCIENCES 100: 173P-173P, Suppl. 1 2006 [Abstract]
40.	Matsumoto T, Ikemoto K, Shiraishi H, et al. Effect of inhibitors of tetrahydrobiopterin (BH4) biosynthesis on vascular cell adhesion molecule-1 (VCAM-1) expression 79th Annual Meeting of the Japanese-Pharmacological-Society, MAR 08-10, 2006 JOURNAL OF PHARMACOLOGICAL SCIENCES 100: 106P-106P, Suppl. 1 2006 [Abstract]
41.	Porkert M, Sher S, Reddy U, et al. Tetrahydrobiopterin: A novel anti-hypertensive therapy 55th Annual Scientific Session of the American-College-of-Cardiology, MAR 11-14, 2006 JOURNAL OF THE AMERICAN COLLEGE OF CARDIOLOGY 47 (4): 371A-371A, Suppl. A FEB 21 2006 [Abstract]
42.	Zheng JS, Hong H, Majid A, et al. Inhibition of brain GTP cyclohydrolase I and tetrahydrobiopterin attenuates cerebral infarction via reducing iNOS and peroxynitrite in ischemic stroke 18th World Congress of Neurology, NOV 05-11, 2005 JOURNAL OF THE NEUROLOGICAL SCIENCES 238: S388-S389, Suppl. 1 NOV 15 2005 [Abstract]
43.	Heales SJR, Foxton RH, Canevari LC, et al. Correction of tetrahydrobiopterin deficiency - Implications for dopa responsive dystonia and other inherited disorders of tetrahydrobiopterin metabolism 18th World Congress of Neurology, NOV 05-11, 2005 JOURNAL OF THE NEUROLOGICAL SCIENCES 238: S322-S322, Suppl. 1 NOV 15 2005 [Abstract]
44.	Cai H, Laude K, Blair J, et al. Recoupling of eNOS in hypertension: Effects of tetrahydrobiopterin and blockade of vascular NAD(P)H oxidases Experimental Biology 2006 Meeting, APR 01-05, 2006 FASEB JOURNAL 20 (5): A1453-A1453, Part 2 MAR 7 2006 [Abstract]
45.	Peterson TE, d'Uscio LV, Cao S, et al. Tetrahydrobiopterin synthesis in endothelial cells is regulated by caveolin-1 Experimental Biology 2006 Meeting, APR 01-05, 2006 FASEB JOURNAL 20 (5): A1076-A1076, Part 2 MAR 7 2006 [Abstract]
46.	Taylor SY, Moat SJ, Lewis MJ, et al. Folic acid protects the endothelial nitric oxide synthase dimer in the face of tetrahydrobiopterin depletion 7th Annual Conference on Arteriosclerosis, Thrombosis and Vascular Biology, APR 27-29, 2006 ARTERIOSCLEROSIS THROMBOSIS AND VASCULAR BIOLOGY 26 (5): E90-E90, MAY 2006 [Abstract]
47.	Khoo J, Bursill C, Cai S, et al. Increased atherosclerosis by endothelial nitric oxide synthase uncoupling from tetrahydrobiopterin deficiency Annual Scientific Conference of the British-Society-Promoting-Cardiovascular-Health, APR 24-27, 2006 HEART 92: A111-A111, Suppl. 2 MAY 2006 [Abstract]
48.	Ali Z, Tatham A, Bendall J, et al. Increased endothelial tetrahydrobiopterin synthesis reduces vein graft accelerated atherosclerosis in apolipoprotein E-knockout mice Annual Scientific Conference of the British-Society-Promoting-Cardiovascular-Health, APR 24-27, 2006 HEART 92: A110-A111, Suppl. 2 MAY 2006 [Abstract]
49.	Antoniades C, Shirodaria C, Leeson P, et al. 5-methyl-tetrahydrofolic acid increases nitric oxide bioavailability and decreases superoxide production by improving eNOS coupling in human vessels in vivo: Effects on intracellular tetrahydrobiopterin oxidation Annual Scientific Conference of the British-Society-Promoting-Cardiovascular-Health, APR 24-27, 2006 HEART 92: A109-A109, Suppl. 2 MAY 2006 [Abstract]
50.	Hayashi T, Miyazaki A, Iguchi A 17 beta-estradiol restores impaired endothelial no bioavailability in hyperglycemia: The relevance of ENOS and tetrahydrobiopterin Annual Meeting of the American-Geriatrics-Society, MAY 03-07, 2006 JOURNAL OF THE AMERICAN GERIATRICS SOCIETY 54 (4): S57-S57, Suppl. S APR 2006 [Abstract]
51.	Stevens, L. M., S. Fortier, M. C. Aubin, I. El-Hamamsy, S. Maltais, M. Carrier and L. P. Perrault (2006). "Effect of tetrahydrobiopterin on selective endothelial dysfunction of epicardial porcine coronary arteries induced by cardiopulmonary bypass." Eur J Cardiothorac Surg 30(3): 464-71.
52.	Pignitter, M., A. C. Gorren, S. Nedeianu, K. Schmidt and B. Mayer (2006). "Inefficient spin trapping of superoxide in the presence of nitric-oxide: Implications for studies on nitric-oxide synthase uncoupling." Free Radic Biol Med 41(3): 455-63.
53.	Lao, H. C., C. L. Huang, P. S. Tsai, L. P. Yan, X. H. Ze and C. J. Huang (2006). "Pre-treatment of acupuncture stimulation of ST36 (Zusanli) significantly attenuates CAT-2, CAT-2B and GTPCH transcription in septic rat lungs." Acta Anaesthesiol Taiwan 44(2): 83-91.
54.	Pandya, M. J., G. Golderer, E. R. Werner and G. Werner-Felmayer (2006). "Interaction of human GTP cyclohydrolase I with its splice variants." Biochem J 400(1): 75-80.
55.	Pangkanon, S., W. Charoensiriwatanamsc and S. Liamsuwanmd (2006). "6-pyruvoyltetrahydropterin synthase deficiency two-case report." J Med Assoc Thai 89(6): 872-7.
56.	Kato, T., H. Sawada, T. Yamamoto, K. Mase and M. Nakagoshi (2006). "Pigment pattern formation in the quail mutant of the silkworm, Bombyx mori: parallel increase of pteridine biosynthesis and pigmentation of melanin and ommochromes." Pigment Cell Res 19(4): 337-345.
57.	Maglione, M., M. Hermann, P. Hengster, S. Schneeberger, W. Mark, P. Obrist, G. Werner-Felmayer, E. R. Werner, R. Margreiter and G. Brandacher (2006). "Tetrahydrobiopterin Attenuates Microvascular Reperfusion Injury Following Murine Pancreas Transplantation." Am J Transplant 6(7): 1551-1559.
58.	Hagenah, J. M., K. Hedrich, B. Becker, P. P. Pramstaller, G. Seidel and C. Klein (2006). "Distinguishing early-onset PD from dopa-responsive dystonia with transcranial sonography." Neurology 66(12): 1951-2.
59.	Matei, V., A. Rodriguez-Vilarrupla, R. Deulofeu, D. Colomer, M. Fernandez, J. Bosch and J. C. Garcia-Pagan (2006). "The eNOS cofactor tetrahydrobiopterin improves endothelial dysfunction in livers of rats with CCl(4) cirrhosis." Hepatology 44(1): 44-52.
60.	Li, H., K. Witte, M. August, I. Brausch, U. Godtel-Armbrust, A. Habermeier, E. I. Closs, M. Oelze, T. Munzel and U. Forstermann (2006). "Reversal of endothelial nitric oxide synthase uncoupling and up-regulation of endothelial nitric oxide synthase expression lowers blood pressure in hypertensive rats." J Am Coll Cardiol 47(12): 2536-44.
61.	Eells, J. B., J. A. Misler and V. M. Nikodem (2006). "Reduced tyrosine hydroxylase and GTP cyclohydrolase mRNA expression, tyrosine hydroxylase activity, and associated neurochemical alterations in Nurr1-null heterozygous mice." Brain Res Bull 70(2): 186-95.
62.	Deng, X. L., X. C. Zhang, F. Zhang, R. Y. Li, H. J. Lu, W. Q. He, L. G. Liu, B. Fan and X. Y. Hu (2006). "Cloning and sequencing of the GTP cyclohydrolase I function region of azole target enzyme gene in artificially induced resistant Candida albicans." Beijing Da Xue Xue Bao 38(3): 301-4. [Article in Chinese]
63.	Okumura, M., M. Masada, Y. Yoshida, H. Shintaku, M. Hosoi, N. Okada, Y. Konishi, T. Morikawa, K. Miura and M. Imanishi (2006). "Decrease in tetrahydrobiopterin as a possible cause of nephropathy in type II diabetic rats." Kidney Int.Advance online publication, 14 June 2006; doi:10.1038/sj.ki.5000431.
64.	Valent, S. and M. Toth (2006). "Activation energy determinations suggest that thiols reverse autooxidation of tetrahydrobiopterin by a different mechanism than ascorbate." Int J Biochem Cell Biol 38(10): 1786-93.
65.	Chavan, B., J. M. Gillbro, H. Rokos and K. U. Schallreuter (2006). "GTP Cyclohydrolase Feedback Regulatory Protein Controls Cofactor 6-Tetrahydrobiopterin Synthesis in the Cytosol and in the Nucleus of Epidermal Keratinocytes and Melanocytes." J Invest Dermatol. Advance online publication, 15 June 2006; doi:10.1038/sj.jid.5700425.
66.	Wang, L., W. Yu, X. Li, C. He, M. Chang, M. Shen, S. Zhao, G. Fu, S. Shen, T. Liu and K. Hsiao (2006). "Study on tetrahydrobiopterin deficiency in Northern Chinese population." Zhonghua Yi Xue Yi Chuan Xue Za Zhi 23(3): 275-9. [Chinese]
67.	Higashi, Y., S. Sasaki, K. Nakagawa, M. Kimura, K. Noma, K. Hara, D. Jitsuiki, C. Goto, T. Oshima, K. Chayama and M. Yoshizumi (2006). "Tetrahydrobiopterin improves aging-related impairment of endothelium-dependent vasodilation through increase in nitric oxide production." Atherosclerosis 186(2): 390-5.
68.	Nagata, D., M. Takahashi, K. Sawai, T. Tagami, T. Usui, A. Shimatsu, Y. Hirata and M. Naruse (2006). "Molecular mechanism of the inhibitory effect of aldosterone on endothelial NO synthase activity." Hypertension 48(1): 165-71.
69.	Abreu-Gonzalez, P., T. Gonzalez-Hernandez, D. Afonso-Oramas, I. Cruz-Muros, P. Barroso-Chinea and M. C. Gonzalez (2006). "Tetrahydrobiopterin stimulates L-DOPA release from striatal tissue." Eur J Pharmacol 541(1-2): 33-7.
70.	Dunbar, A. Y., G. J. Jenkins, S. Jianmongkol, M. Nakatsuka, E. R. Lowe, M. Lau and Y. Osawa (2006). "Tetrahydrobiopterin protects against guanabenz-mediated inhibition of neuronal nitric-oxide synthase in vitro and in vivo." Drug Metab Dispos 34(9): 1448-56.
71.	Linscheid, P., D. Seboek, H. Zulewski, A. Scherberich, N. Blau, U. Keller and B. Müller (2006). "Inflammation-mediated metabolic effect do not involve endogenous nitric oxide in human adipocytes." AJP 290: 1068-1077.
72.	Swick, L. and G. Kapatos (2006). "A yeast 2-hybrid analysis of human GTP cyclohydrolase I protein interactions." J Neurochem 97(5): 1447-55.
73.	Yamashiro, S., Y. Kuniyoshi, K. Arakaki, T. Uezu, K. Miyagi and K. Koja (2006). "Cardioprotective effects of tetrahydrobiopterin in cold heart preservation after cardiac arrest." Ann Thorac Cardiovasc Surg 12(2): 95-104.
74.	Kim, S. U., I. H. Park, T. H. Kim, K. S. Kim, H. B. Choi, S. H. Hong, J. H. Bang, M. A. Lee, I. S. Joo, C. S. Lee and Y. S. Kim (2006). "Brain transplantation of human neural stem cells transduced with tyrosine hydroxylase and GTP cyclohydrolase 1 provides functional improvement in animal models of Parkinson disease." Neuropathology 26(2): 129-40.
75.	Grobe, A. C., S. M. Wells, E. Benavidez, P. Oishi, A. Azakie, J. R. Fineman and S. M. Black (2006). "Increased oxidative stress in lambs with increased pulmonary blood flow and pulmonary hypertension: role of NADPH oxidase and endothelial NO synthase." Am J Physiol Lung Cell Mol Physiol 290(6): L1069-77.
76.	Akamine, E. H., E. M. Kawamoto, C. Scavone, D. Nigro, M. H. Carvalho, A. T. R. de Cassia, L. R. Britto and Z. B. Fortes (2006). "Correction of Endothelial Dysfunction in Diabetic Female Rats by Tetrahydrobiopterin and Chronic Insulin." J Vasc Res 43(4): 309-320.
77.	Hjermind, L. E., L. G. Johannsen, N. Blau, R. A. Wevers, C. B. Lucking, J. M. Hertz, L. Friberg, L. Regeur, J. E. Nielsen and S. A. Sorensen (2005). "Dopa-responsive dystonia and early-onset Parkinson's disease in a patient with GTP cyclohydrolase I deficiency?" Mov Disord. 21:679-682
78.	Urano, F., N. Hayashi, F. Arisaka, H. Kurita, S. Murata and H. Ichinose (2006). "Molecular mechanism for pterin-mediated inactivation of tyrosine hydroxylase: formation of insoluble aggregates of tyrosine hydroxylase." J Biochem (Tokyo) 139(4): 625-35.
79.	Nandi, M., J. Leiper, F. Arrigoni, A. Hislop, P. Vallance and S. Haworth (2006). "Developmental regulation of GTP-CH1 in the porcine lung and its relationship to pulmonary vascular relaxation." Pediatr Res 59(6): 767-72.
80.	Serova, L. I., M. Filipenko, N. Schilt, M. Veerasirikul and E. L. Sabban (2006). "Estrogen-triggered activation of GTP cyclohydrolase 1 gene expression: role of estrogen receptor subtypes and interaction with cyclic AMP." Neuroscience 140(4): 1253-63.
81.	Lam, K. K., Y. M. Lee, G. Hsiao, S. Y. Chen and M. H. Yen (2006). "Estrogen therapy replenishes vascular tetrahydrobiopterin and reduces oxidative stress in ovariectomized rats." Menopause 13(2): 294-302.
82.	Hertz, J. M., K. Ostergaard, I. Juncker, S. Pedersen, A. Romstad, L. B. Moller, F. Guttler and E. Dupont (2006). "Low frequency of Parkin, Tyrosine Hydroxylase, and GTP Cyclohydrolase I gene mutations in a Danish population of early-onset Parkinson's Disease." Eur J Neurol 13(4): 385-90.
83.	Lopez-Laso, E., A. Ormazabal, R. Camino, F. J. Gascon, J. J. Ochoa, M. E. Mateos, M. J. Munoz, J. L. Perez-Navero, J. I. Lao, M. A. Vilaseca and R. Artuch (2006). "Oral phenylalanine loading test for the diagnosis of dominant guanosine triphosphate cyclohydrolase 1 deficiency." Clin Biochem 39(9): 893-7.
84.	Huang, Y. Z., I. Trender-Gerhard, M. J. Edwards, P. Mir, J. C. Rothwell and K. P. Bhatia (2006). "Motor system inhibition in dopa-responsive dystonia and its modulation by treatment." Neurology 66(7): 1088-90.
85.	Chen, X., B. Gao, X. Y. Jia, C. Su, Y. P. Lu, Z. Y. Wang, X. P. Fan, B. Xiao and J. Z. Liu (2006). "High-level expression of phenylalanine ammonia-lyase in Lactococcus Lactis via synthesized sequence based on bias codons." Sheng Wu Gong Cheng Xue Bao 22(2): 187-90 [Article in Chinese].
86.	Wang, L., W. M. Yu, C. He, M. Chang, M. Shen, Z. Zhou, Z. Zhang, S. Shen, T. T. Liu and K. J. Hsiao (2006). "Long-term outcome and neuroradiological findings of 31 patients with 6-pyruvoyltetrahydropterin synthase deficiency." J Inherit Metab Dis 29(1): 127-34.
87.	Leuzzi, V., C. Carducci, C. Carducci, F. Chiarotti, C. Artiola, T. Giovanniello and I. Antonozzi (2006). "The spectrum of phenylalanine variations under tetrahydrobiopterin load in subjects affected by phenylalanine hydroxylase deficiency." J Inherit Metab Dis 29(1): 38-46.
88.	Forstermann, U. and T. Munzel (2006). "Endothelial nitric oxide synthase in vascular disease: from marvel to menace." Circulation 113(13): 1708-14.
89.	Takanashi J, Kanazawa M, Kohno Y. Central tegmental tract involvement in an infant with 6-pyruvoyltetrahydropterin synthetase deficiency. AJNR Am J Neuroradiol 2006;27(3):584-5.
90.	Ding Z, Georgiev P, Thony B. Administration-route and gender-independent long-term therapeutic correction of phenylketonuria (PKU) in a mouse model by recombinant adeno-associated virus 8 pseudotyped vector-mediated gene transfer. Gene Ther 2006;13(7):587-93.
91.	1. Hara Y, Teramoto K, Ishidate K, Arii S. Cytoprotective function of tetrahydrobiopterin in rat liver ischemia/reperfusion injury. Surgery 2006;139(3):377-84.
92.	Furukawa, Y. (2006). "Dopa-responsive dystonia: clinical, genetic, and biochemical studies." Rinsho Shinkeigaku 46(1): 19-34.[Article in Japanese]
93.	Yang, S., Y. J. Lee, J. M. Kim, S. Park, J. Peris, P. Laipis, Y. S. Park, J. H. Chung and S. P. Oh (2006). "A murine model for human sepiapterin-reductase deficiency." Am J Hum Genet 78(4): 575-87.
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